Askin瘤的螺旋CT表现

目的:评价Askin瘤的螺旋CT表现,提高对此病的认识及鉴别诊断能力。方法:回顾性分析经病理证实的20例Askin瘤的螺旋CT表现。结果:依据发病部位的不同,将20例Askin瘤分为2型:即胸壁型和纵隔型。胸壁型16例,纵隔型4例。胸壁Askin瘤表现为起源于胸壁的软组织肿物,14例病灶较大且密度不均匀,可见囊变、坏死区,2例病灶较小且密度均匀。肋骨破坏11例,胸腔积液10例,2例出现肺部、骨骼转移,2例肿瘤出现钙化。纵隔Askin瘤分别表现为起源于纵隔的不均匀密度软组织肿物,其中3例已经侵犯前胸壁。结论:Askin瘤多表现为侵犯胸壁、纵隔的恶性软组织肿物,密度多不均匀,多伴有肋骨破坏、胸腔积液。对发生于儿童及青少年的胸壁、纵隔恶性肿物,进行鉴别诊断时要考虑此病。 

Spiral CT Manifestations of Askin Tumor

Objective: To describe the spiral CT appearances of Askin tumors and to facilitate the understanding and differential diagnosis of Askin tumors. Materials: The CT features of twenty pathology-confirmed Askin tumors were reviewed retrospectively. Results: Based on the locations of lesions, 20 Askin tumors were divided into two groups, including sixteen Askin tumors of the chest wall, four Askin tumors of the mediastinum. Askin tumors of the chest wall were soft tissue mass originated from the chest wall. Fourteen tumors were large with heterogeneous density which showed cystic degeneration and necrosis on CT scans. Two tumors were small with homogeneous density. CT scans showed rib destruction in eleven cases, pleural effusion in ten cases, lung and bone metastasis in two patients, and calcification in two tumors. Askin tumor of the mediastinum was seen as soft tissue mass with heterogeneous density originated from mediastinum. Askin tumor of the mediastinum showed anterior chest wall invasion. Conclusion: Askin tumors showed soft tissue mass with heterogeneous density in the chest wall or the mediastinum on CT scans, usually accompanied with rib destruction and pleural effusion. Askin tumor should be considered in children and teenagers as a differential diagnosis for soft-tissue mass in the chest wall or the mediastinum.